Lymphomatoid Granulomatous: Pulmonary Manifestations Of A Rare Entity
DOI:
https://doi.org/10.53555/jaz.v44iS7.3130Keywords:
Lymphomatoid granulomatosis, Bilateral pulmonary cavities, RX, CtAbstract
Background: Lymphomatoid granulomatosis (LG) is a rare lymphoproliferative disease predominantly affecting extranodal sites, characterized by its angiocentric lymphoma nature and a notable affinity for blood vessels.
Objective: To highlight the clinical and radiographic features of LG, emphasizing its primary pulmonary involvement.
Methods: A case report of a 69-year-old male presenting with distinct radiographic findings via conventional chest radiography (XR) and computed tomography (CT).
Results: The patient exhibited multiple bilateral cavitated nodular lesions in both XR and CT scans. Despite the diagnostic challenges and a grim clinical course, the disease was confirmed as LG post-mortem.
Conclusion: Recognizing LG's distinctive pulmonary manifestations within an appropriate clinical context is pivotal for early diagnosis and intervention, albeit with a median survival of approximately 2 years
Downloads
References
Aromolo, I. F., et al. (2023). "The Bowel-Associated Arthritis–Dermatosis Syndrome (BADAS): A Systematic Review." Metabolites 13(7): 790.
Derbyshire, J., et al. (2023). "EBV Positive Lymphomatoid Granulomatosis Following Dental Extractions." Ear, Nose & Throat Journal 102(4): NP154-NP156.
Girard, N. (2023). Malignant Mimics of Orphan Lung Diseases. Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease, Springer: 777-790.
Kobets, A. J., et al. (2023). "STAT5b gain-of-function disease in a child with mycobacterial osteomyelitis of the skull: rare presentation of an emerging disease entity." Child's Nervous System: 1-7.
Pina-Oviedo, S., et al. (2023). Pulmonary Lymphoproliferative Disorders. The Thorax: Medical, Radiological, and Pathological Assessment, Springer: 477-564.
Quintanilla-Martinez, L., et al. (2023). "New concepts in EBV-associated B, T, and NK cell lymphoproliferative disorders." Virchows Archiv 482(1): 227-244.
Razack, R., et al. (2023). "Epstein-Barr Virus-positive Mucocutanous Ulcer of the Uterine Cervix: Report of a Rare and Evolving Entity." International Journal of Gynecological Pathology 42(1): 21-25.
Singh, G., et al. (2023). "An Update on WHO Classification of Thoracic Tumours 2021-Newly Described Entities and Terminologies." JOURNAL OF CLINICAL AND DIAGNOSTIC RESEARCH 17(6): EE01-EE05.
So, M., et al. (2023). "Pulmonary lymphomatoid granulomatosis in a patient with long-term use of a tumour necrosis factor-α inhibitor." BMJ Case Reports CP 16(5): e254211.
Tehzeeb, J., et al. (2023). "A 21-Year-Old Hispanic Woman Presenting With Cutaneous and Pulmonary Nodules." Chest 163(4): e167-e171.
Downloads
Published
Issue
Section
License
Copyright (c) 2023 Abdullahi Abdirahim Hussein, Warda Khan, Shaukat Ullah, Dr. Rimaa Mohammad Ibrahim Lafi, Dr. Mohammad Othman Mohammad Ibrahim Lafi, Muhammad Imran Ul Haq
This work is licensed under a Creative Commons Attribution 4.0 International License.
