Lymphomatoid Granulomatous: Pulmonary Manifestations Of A Rare Entity
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Abstract
Background: Lymphomatoid granulomatosis (LG) is a rare lymphoproliferative disease predominantly affecting extranodal sites, characterized by its angiocentric lymphoma nature and a notable affinity for blood vessels.
Objective: To highlight the clinical and radiographic features of LG, emphasizing its primary pulmonary involvement.
Methods: A case report of a 69-year-old male presenting with distinct radiographic findings via conventional chest radiography (XR) and computed tomography (CT).
Results: The patient exhibited multiple bilateral cavitated nodular lesions in both XR and CT scans. Despite the diagnostic challenges and a grim clinical course, the disease was confirmed as LG post-mortem.
Conclusion: Recognizing LG's distinctive pulmonary manifestations within an appropriate clinical context is pivotal for early diagnosis and intervention, albeit with a median survival of approximately 2 years
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